Lymphangioleiomyomatosis

Lymphangioleiomyomatosis is indexed under Respiratory, Rare Lung Disease. Also known as LAM.

US prevalence

~3.4-7.8 per million women Source: LAM Foundation; ATS. This figure comes from a professional society, registry, or study rather than a federal source. Label: REPORTED.

ICD-10-CM codes

J84.81

Typical onset

Women 20-40

Course

progressive

Body systems

pulmonary, renal

Sex differences

Almost exclusively women (estrogen-driven)

Racial and ethnic differences

Pan-ethnic

What this page does not establish

These figures describe populations, not individuals, and none of them is a diagnosis or a treatment recommendation. Prevalence estimates are approximate and reflect published ranges. Disparity figures are reported patterns, not causes.

Taxonomy last reviewed 2026-05-19. Each figure on the interactive page carries its own source and retrieval date, which can be later than this review.

Browse all indexed conditions · Source registry · Methodology · Known limitations