Granulomatosis with Polyangiitis

Granulomatosis with Polyangiitis is indexed under Autoimmune & Inflammatory, ANCA-Associated Vasculitis. Also known as GPA, Wegener granulomatosis (former), Wegener granulomatosis.

US prevalence

~3 per 100,000 people in the United States Source: MedlinePlus Genetics (NLM), Granulomatosis with polyangiitis, frequency section last updated July 1, 2013. This figure comes from a professional society, registry, or study rather than a federal source. Label: REPORTED.

ICD-10-CM codes

M31.30, M31.31, M31.3

Typical onset

Age 40-65; can occur at any age

Course

managed

Body systems

respiratory, renal, immune, vascular, pulmonary, ENT

Sex differences

M slightly > F

Racial and ethnic differences

More common in Northern European descent; rare in Black and Asian populations

What this page does not establish

These figures describe populations, not individuals, and none of them is a diagnosis or a treatment recommendation. Prevalence estimates are approximate and reflect published ranges. Disparity figures are reported patterns, not causes.

Taxonomy last reviewed 2026-05-19. Each figure on the interactive page carries its own source and retrieval date, which can be later than this review.

Browse all indexed conditions · Source registry · Methodology · Known limitations