Alport Syndrome

Alport Syndrome is indexed under Renal & Urologic, Genetic Kidney Disease. Also known as hereditary nephritis.

US prevalence

~1 in 5,000-10,000 Source: NIH NIDDK; ASN. Cites federal and non-federal sources, and the record does not say which one gave this figure. Label: REPORTED.

ICD-10-CM codes

Q87.81

Typical onset

X-linked: males ESRD by 20s-30s; autosomal recessive variable

Course

progressive

Body systems

renal, audiologic, ophthalmologic

Sex differences

X-linked: males more severe; carrier females variable

Racial and ethnic differences

Pan-ethnic

What this page does not establish

These figures describe populations, not individuals, and none of them is a diagnosis or a treatment recommendation. Prevalence estimates are approximate and reflect published ranges. Disparity figures are reported patterns, not causes.

Taxonomy last reviewed 2026-05-19. Each figure on the interactive page carries its own source and retrieval date, which can be later than this review.

Browse all indexed conditions · Source registry · Methodology · Known limitations